Blue rubber bleb naevus syndrome.
نویسندگان
چکیده
Blue rubber bleb naevus syndrome (BRBNS) is a rare clinical entity characterised by multiple haemangiomas commonly occurring in the skin and the gastrointestinal (Gl) tract. The association between these cutaneous cavernous haemangiomas and similar lesions in the U l tract was first described in 1860 and the acronym B R B N S was given by Bean in 1958 [ l J, Patients may present with massive GI bleeding or anaemia due to chronic occult bleeding.
منابع مشابه
Blue rubber bleb naevus syndrome and Chiari malformation: high risk of peroperative haemorrhage.
Blue rubber bleb naevus syndrome is an uncommon disorder whereby patients possess cutaneous vascular malformations. Cranial malformations have been rarely reported in the literature. We report the first ever case of a patient with blue rubber bleb naevus syndrome (BRBNS), who was found to have a symptomatic Chiari malformation and prominent subcutaneous vascular malformations in communication w...
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Blue rubber bleb nevus syndrome is a sporadic disease with widely distributed dark blue papules and nodules and soft skin-colored compressible protuberances (rubber blebs) as well as large vascular malformations. Gasterointestinal lesions are documented by upper endoscopy and colonoscopy; hemorrhages from these lesions create irondeficinecy anemia. Other sites of visceral involvement are less c...
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A 71-year-old woman with the blue rubber bleb naevus syndrome experienced 4 episodes of self-limiting unilateral exophthalmos. Is is suggested that a vascular malformation in the orbit is responsible for this phenomenon. A biopsy sample was taken of one of the cutaneous lesions and studied by light and transmission electron microscopy. The histological appearances are discussed in relation to p...
متن کاملThe value of double balloon enteroscopy in diagnosing blue rubber bleb naevus syndrome: a case report
Blue rubber bleb naevus syndrome is a rare vascular disorder associated with multiple gastrointestinal haemangiomas that have the potential for life-threatening haemorrhage. These may be difficult to diagnose, and have classically been described using computed tomographic studies and/or mesenteric angiography. Resected surgical specimens of these lesions, especially in the small bowel, have oft...
متن کاملSynchronous multiple small bowel intussusceptions in an adult with blue rubber bleb naevus syndrome: Report of a case and review of literature
BACKGROUND Blue rubber bleb naevus syndrome (BRBNS), is an uncommon condition characterised by cavernous haemangiomas of skin and gastrointestinal tract. The most common complication of this syndrome is gastrointestinal bleeding. Intussusception of bowel, although a known complication, has rarely been reported. CASE PRESENTATION We report the case of a 37-year-old man who presented with multi...
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ورودعنوان ژورنال:
- The Ceylon medical journal
دوره 52 4 شماره
صفحات -
تاریخ انتشار 2001